V. Special Populations
E. Sickle Cell Disease
This section includes physician
and patient resource guides in pain management in sickle cell
well as clinical pathways for treatment. Videos and guidelines
for treatment are also available.
Darbarai, D. S., Ballas, S. K., &
Clauw, D. J. (2014).
Thinking beyond sickling to better understand pain in sickle
cell disease. European Journal of Haematology, 93(2), 89-95. DOI:
Darbari, D. S., Neely, M., van den Anker, J., & Rana, S.
Increased clearance of morphine in sickle cell
disease: Implications for
pain management. The Journal of Pain, 12(5), 531-538. DOI:
Perioperative care of the patient with sickle cell disease. AORN
Journal, 93(1), 150-159.
M. M., DeBaun, M. R., & Frei-Jones, M. (2011).
Multi-modal intervention for the
management of sickle cell pain significantly decreases the rate of
acute chest syndrome. Pediatric Blood Cancer, 56, 262-266.
Brandow, A. M.,
Weisman, S. J., & Panepinto, J. A. (2011).
The impact of a multidisciplinary
model on sickle cell disease pain hospitalizations. Pediatric
Blood Cancer, 56, 789-793. DOI:
Ameringer, S. &
Smith, W. R. (2011).
Emerging biobehavioral factors of fatigue in sickle cell
disease. Journal of Nursing Scholarship, 43(1), 22-29. DOI:
Hope and Destiny: A Patient's and Parent's Guide to Sickle Cell Anemia
and Sickle Cell Trait, 3rd Edition
Platt, Jr., A. F.,
Eckman, J., & Hsu, L. (2011). IN: Hilton Publishing. ISBN:
Navaid, M. & Melvin, T. (2010).
A palliative care approach in treating patients
with sickle cell disease using
exchange transfusion. American Journal of
Hospice & Palliative Medicine, 27(3), 215-218.
Wright, J. & Ahmedzai, S. H. (2010).
management of painful crisis in sickle cell disease. Current Opinion in
Supportive and Palliative Care, 4, 97-106. DOI:
Ballas, S. K., Bauserman, R. L., McCarthy, W. F.,
Castro, O. L. Smith, W. R. & Waclawiw, M. A. (2010).
Hydroxyurea and acute
painful crises in sickle cell anemia: Effects on hospital length of stay and
during hospitalization, outpatient acute care contacts, and
at home. Journal of Pain and Symptom Management, 40(6), 870-882.
Edwards, L. Y. & Edwards, C. L. (2010).
Psychosocial treatments in pain management of sickle cell disease. Journal of
the National Medical Association, 102(11), 1084-1094.
Wilkie, D. J., Johnson, B., Mack, A. K., Labotka,
R., & Molokie, R. E. (2010).
Sickle cell disease: An opportunity
care across the life span. Nursing Clinics of North America, 45, 375-397.
13. Hyacinth, H. I,
Gee, B. E., & Hibbert, J. M. (2010).
The role of nutrition in sickle cell disease. Nutrition and Metabolic
Insights, 3, 56-67. DOI: 10.4137/NMI.S5048.
14. Zempsky, W. T., Loiselle, K. A., McKay, K., Lee.
B. H., Hagstrom, J. N., & Schechter, N. L. (2010).
with sickle cell
disease receive disparate care for pain in the emergency department? The
Journal of Emergency Medicine, 39(5), 691-695.
Mousa, S. A.,Al Momen, A., Al Sayegh, F., Al
Jaouni, S., Nasrullah, Z., Al Saeed, H., et al. (2010).
of painful vaso-occlusive crisis of sickle-cell anemia: Consensus opinion. Clinical and
Applied Thrombosis/Hemostasis, 16(4), 365-376. DOI:
16. Dampier, C., Lieff, S., LeBeau, P. Rhee, S.,
McMurray, M., Rogers, Z., et al. (2010).
Health-related quality of life
children with sickle cell disease: A report from the Comprehensive Sickle Cell
Centers Clinical Trial Consortium. Pediatric Blood Cancer, 55, 485-494.
17. Odesina, V., Bellini, S., Leger, R., Bona, R.,
Delaney, C., Andemariam, B., et al. (2010).
management in the emergency department. Advanced Emergency Nursing Journal,
18. Solomon, L. R. (2010).
Pain management in adults with sickle cell disease in a medical center emergency
department. Journal of the National Medical Association, 102(1),
19. Taylor, L. E. V., Stotts, N. A., Humphreys, J.,
Treadwell, M. J., & Miaskowski, C. (2010).
A review of the
literature on the
multiple dimensions of chronic pain in adults with sickle cell disease.
Journal of Pain and Symptom Management, 40(3), 416-435.
20. Wilkie, D. J., Molokie, R., Boyd-Seal, D.,
Suarez, M. L., Kim, Y. O., Zong, S., et al. (2010).
Patient-reported outcomes: Descriptors of nociceptive and neuropathic pain and
barriers to effective pain management in adult outpatients with sickle cell
disease. Journal of the National Medical Association, 102(1), 18-27.
21. Sickle Cell Anemia: A Motherís Perspective What Every Parent Should Know
Lipscome, M & Chamberlin, M. (2010). CreateSpace. ISBN: 978-1456450670.
Century Ultimate Medical Guide to Sickle Cell Anemia - Authoritative
Clinical Information for Physicians and Patients (Two CD Set)
US Government. (2009). FL: Progressive Management. ISBN: 978-1422023105.
Miscola, P. Sorrentino, F., Scaramucci, L., de
Fabritiis, P., Cianciulli, P. (2009).
Pain syndromes in sickle cell
update. Pain Medicine, 10(3), 470-480.
Cotton, S., Grossoehme, D., Rosenthan, S. L.,
McGrady, M. E., Roberts, Y. H., Hines, J., et al. (2009).
coping in adolescents with sickle cell disease: A pilot study. Journal of
Pediatric Hematology Oncology, 31(5), 313-318.
Howard, J., Thomas, V. J., & Rawle, H. M. (2009).
Pain management and quality of life in sickle cell disease. Expert Reviews
Pharmacoeconomics Outcomes, Research, 9(4), 347-352. DOI:
McClellan, C. B., Schatz, J. C., Puffer, E.,
Sanchez, C. E., Stancil, M. T., & Roberts, C. W. (2009).
wireless technology for a home-based sickle cell pain management protocol.
Journal of Pediatric Psychology, 34(5), 564-573. DOI:
OíConnell-Edwards, C. F., Edwards, C. L., Pearce,
M., Wachholtz, A. B., Wood, M., Muhammad, M., et al. (2009).
and pain associated with sickle cell disease: Exploration of a non-linear model. Journal of African American Studies, 13, 1-13.
Field, J. J., Knight-Perry, J.
E., & DeBaun, M. R. (2009).
Acute pain in children and adults
with sickle cell
disease: Management in the absence of
evidence-based guidelines. Current Opinion in Hematology, 16,
Mann-Jiles, V. & Morris, D. L. (2009).
life of adult patients with sickle cell disease. Journal of the American
Academy of Nurse Practitioners, 21, 349-349.
Benjamin, L. (2008).
Pain management in sickle cell disease: Palliative care begins at birth?
Hematology/the Education Program of the American Society of Hematology,
Barakat, L. P., Patterson, C. A., Daniel, L. C.,
& Dampier, C. (2008).
Quality of life among adolescents with sickle cell disease: Mediation of pain by
internalizing symptoms and parenting distress. Health and Quality of Life
Outcomes, 6, (60), 1-9.
The Sickle Cell
Information Center - Georgia Comprehensive Sickle Cell Center, Atlanta, GA.
- The Management of Sickle Cell Disease - National Institute of Health
- Sickle Cell Pain
Relief Record - St. Francis Hospital & Medical Center, Hartford, CT.
Other Organizational Links
American Academy of Pediatrics Policy Statements
Health Supervision for Children with Sickle Cell Disease
Timely and appropriate treatment of SCD is critical, because
life-threatening complications develop rapidly. It is essential that
every child with SCD receive comprehensive care that is coordinated
through a medical home with appropriate expertise.
Website last modified:
February 16, 2015